Document Type : Case Reports
Authors
- Mohammad Vaseie 1
- Mahsa Soti Khiabani 2
- Maryam Monajemzadeh 3
- Hojatollah Raji 4
- Fatemeh Zamani 5
- Neda Pak 6
1 Department of Emergency Medicine, Faculty of Medicine, Tehran University of Medical Sciences, Tehran, Iran
2 1-Children’s Medical Center, Pediatrics Center of Excellence, Tehran, Iran 2- Pediatric Emergency Department, Tehran University of Medical Sciences, Tehran, Iran
3 1. Pathology Department, Children Medical Center, Tehran University of Medical Sciences, Tehran, Iran 2. Pediatric Gastroenterology and Hepatology Research Center, Pediatrics Centre of Excellence, Children’s Medical Center, Tehran
4 1- Children’s Medical Center, Pediatrics Center of Excellence, Tehran, Iran 2- Department of Pediatric Surgery, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, Iran
5 1.Department of Radiology, Children Medical Center of Excellence, Tehran University of Medical Science, Tehran, Iran 2.Advanced Diagnostic and Interventional Radiology Research Center, Tehran University of Medical Sciences, Tehran, Iran
6 Department of Radiology, Children Medical Centre of Excellence, Tehran University of Medical Sciences, Tehran, Iran
Abstract
The occurrence of rectosigmoid junction inflammatory myofibroblastic tumor IMT is uncommon in children. This is a rare form of mesenchymal tumor, belonging to the category of soft tissue tumors, and can be found at any anatomical site from the central nervous system to the gastrointestinal tract.
Our patient was a 10-year-old male subject complaining of lack of defecation and constipation. The patient had decreased the frequency of defecation and constipation about two weeks before his referral and had not improved despite the use of laxatives. The abdomen was completely distended and there was no tenderness or guarding in the examination. Several airfluid levels are shown on the abdominal X-ray. In the ultrasound, free fluid was reported in the interlobular and pelvic spaces. The patient was transferred into the operating room. A tumor of the rectosigmoid junction was detected. The pathology showed evidence of IMT.
IMT is a rare neoplastic tumor of unknown origin which may be present at various sites in the body. Complete surgical removal is usually curative, but early detection of recurrence is required. Treatment options include chemotherapy, radiation therapy, and immunotherapy, and further research is needed to improve the understanding and management of this rare tumor.
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