Document Type : Case Reports


1 Cutaneous Leishmaniosis Research Center, Mashhad University of Medical Sciences, Mashhad, Iran

2 Department of Pathology, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran

3 Student Research Committee, School of Medicine, Shahrood University of Medical Sciences, Shahrood, Iran


Syringocystadenoma papilliferum is a rare benign adnexal tumor that originates from the apocrine and eccrine glands. It mainly manifests as a solitary lesion in the head and neck; however, rarely, it may involve the trunk and limbs, typically with a linear pattern. Here, we report an extremely rare case of congenital linear syringocystadenoma papilliferum on the left buttock near the anus in a 6-year-old girl. This lesion should be considered in the list of differential diagnosis of linear lesions in order to prevent complications with proper diagnosis, treatment or follow-up.


Main Subjects

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