Iranian Journal of Pathology

Gorham’s Disease of the Maxilla and Mandible With Distinctive Cone Beam Computerized Tomographic Features

Document Type : Case Reports

Authors

Rupam Sinha 1
Soumyabrata Sarkar 1
Tanya Khaitan 2
Deepsikha Ramani 1

1 Dept. of Oral Medicine & Radiology, Haldia Institute of Dental Sciences and Research, Haldia, West Bengal, India

2 Dept. of Dentistry, Murshidabad Medical College and Hospital, Berhampore, West Bengal, India

https://doi.org/10.30699/ijp.2017.25855
Abstract
Gorham’s disease is a rare and atypical disorder epitomized by progressive osteolysis of bone with eventual total disappearance of bone. The etiology is poorly understood with variable clinical presentation. Most times it is initially misdiagnosed as temporomandibular joint dysfunction, periodontal disease or odontogenic tumors clinically and radiographically in routine dental practice. Radiographic examination, such as Cone Beam Computerized Tomography (CBCT) play a vital role in diagnosing such disorder resulting in disappearance of the involved bone entirely, which is a definitive distinguishing feature of this condition. Regarding the rarity of the condition, the current study presents a case of Gorham’s disease with distinctive clinical, radiological, and histological, features involving maxilla and mandible.

Keywords

Gorham’s disease
Maxilla
Mandible
Massive Osteolysis
Resorption

Subjects

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Iranian Journal of Pathology
Volume 12, Issue 3
Summer 2017
Pages 301-306

  • Receive Date 27 April 2016
  • Revise Date 20 June 2016
  • Accept Date 23 June 2016

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