Gorham’s Disease of the Maxilla and Mandible With Distinctive Cone Beam Computerized Tomographic Features

Sinha, Rupam; Sarkar, Soumyabrata; Khaitan, Tanya; Ramani, Deepsikha

doi:10.30699/ijp.2017.25855

Document Type : Case Reports

Authors

¹ Dept. of Oral Medicine & Radiology, Haldia Institute of Dental Sciences and Research, Haldia, West Bengal, India

² Dept. of Dentistry, Murshidabad Medical College and Hospital, Berhampore, West Bengal, India

https://doi.org/10.30699/ijp.2017.25855

Abstract

Gorham’s disease is a rare and atypical disorder epitomized by progressive osteolysis of bone with eventual total disappearance of bone. The etiology is poorly understood with variable clinical presentation. Most times it is initially misdiagnosed as temporomandibular joint dysfunction, periodontal disease or odontogenic tumors clinically and radiographically in routine dental practice. Radiographic examination, such as Cone Beam Computerized Tomography (CBCT) play a vital role in diagnosing such disorder resulting in disappearance of the involved bone entirely, which is a definitive distinguishing feature of this condition. Regarding the rarity of the condition, the current study presents a case of Gorham’s disease with distinctive clinical, radiological, and histological, features involving maxilla and mandible.

Keywords

Main Subjects

Oral Pathology

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Iranian Journal of Pathology

Gorham’s Disease of the Maxilla and Mandible With Distinctive Cone Beam Computerized Tomographic Features

References

References

Volume 12, Issue 3
July 2017
Pages 301-306

Gorham’s Disease of the Maxilla and Mandible With Distinctive Cone Beam Computerized Tomographic Features

References

References

Volume 12, Issue 3July 2017Pages 301-306

Volume 12, Issue 3
July 2017
Pages 301-306