Iranian Journal of Pathology

A Tete – a – tete of benign, borderline and malignant fibrohistiocytic tumor

Document Type : Case Reports

Authors

RASHMI M.V. 1
Pavithra P 1
Shivakumarappa G.M. 2

1 Dept. of Pathology, Sri Siddhartha Medical College, Tumkur, Karnataka – 572104, India

2 Dept. of Surgery, Sri Siddhartha Medical College, Tumkur, Karnataka – 572104, India

Abstract
Dermatofibrosarcoma protruberans is a relatively uncommon slow growing, locally aggressive fibrous tumor of the skin. It has a prospensity of progressing to fibrosarcomatous change in 5% of the cases. We present a case of a 56 yr old male with presented to the outpatient department of surgery, Sri Siddhartha Medical College, Tumkur with a chest swelling in 2013. FNAC was inconclusive and the mass was excised. On histopathology, areas of benign fibrohistiocytic tumor, dermatofibrosarcoma protruberans and fibrosarcomatous dermatofibrosarcoma were identified in the same tumor. Immunohistochemistry confirmed the diagnosis of DFSP with fibrosarcomatous change. Although, transformed DFSP is more aggressive, the prognosis is influenced by the extent of excision and with wide excision, there may be little increased risk for recurrence and metastasis over that of conventional DFSP.

Keywords

Benign fibrohistiocytic tumor
Dermatofibrosarcoma protruberans
Fibrosarcomatous dermatofibrosarcoma protruberans
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Iranian Journal of Pathology
Volume 11, Issue 3
Summer 2016
Pages 286-290

  • Receive Date 22 June 2015
  • Revise Date 29 September 2015
  • Accept Date 11 May 2016

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