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Walke, V., Bijwe, S., D’ Costa, G., Jawarkar, A. (2013). Lhermitte – Duclos Disease in a Young Adult: Rare Entity. Iranian Journal of Pathology, 8(3), 194-198.
Vaishali Walke; Sanjay Bijwe; Grace D’ Costa; Aashish Jawarkar. "Lhermitte – Duclos Disease in a Young Adult: Rare Entity". Iranian Journal of Pathology, 8, 3, 2013, 194-198.
Walke, V., Bijwe, S., D’ Costa, G., Jawarkar, A. (2013). 'Lhermitte – Duclos Disease in a Young Adult: Rare Entity', Iranian Journal of Pathology, 8(3), pp. 194-198.
Walke, V., Bijwe, S., D’ Costa, G., Jawarkar, A. Lhermitte – Duclos Disease in a Young Adult: Rare Entity. Iranian Journal of Pathology, 2013; 8(3): 194-198.

Lhermitte – Duclos Disease in a Young Adult: Rare Entity

Article 10, Volume 8, Issue 3, Summer 2013, Page 194-198  XML PDF (482 K)
Authors
Vaishali Walke 1; Sanjay Bijwe2; Grace D’ Costa1; Aashish Jawarkar1
1Dept. of Pathology, Grant Medical College & Sir J. J. Group of Hospitals, Byculla, Mumbai MS – India
2Dept. of Pathology, Grant Medical College & Sir J. J. Group of Hospitals, Byculla, Mumbai MS , India
Abstract
Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of the mass along with shunt drainage was performed. Post operative course was uneventful. Histopathological features confirmed the diagnosis.
 
Keywords
Lhermitte Duclos Disease; Case Report; India
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